Radiology, Vol 125, 769-773, Copyright © 1977 by Radiological Society of North America
Diagnosis oligohydramnios-related pulmonary hypoplasia (Potter syndrome): value of portable voiding cystourethrography in newborns with respiratory distress
EL Wolf, WE Berdon, DH Baker, HJ Wigger and WA Blanc
Potter renal nonfunctional syndrome is an association of facial and limb
anomalies, pulmonary hypoplasia, and fetal renal anomalies which lead to
marked oligohydramnios, including renal agenesis (true Potter syndrome),
renal cystic dysplasia, and obstructive uropathies. Some infants survive
long enough to develop severe respiratory distress secondary to pulmonary
hypoplasia. The underlying renal disease is often noted only at autopsy. We
studied four infants, only one of whom had clinical signs of the renal
nonfunction syndrome. Portable voiding cystourethrography revealed a tiny
bladder in three infants with cystic dysplasia kidneys (two of these
infants had reflux into unused ureters). Bladder hypertrophy and
vesicoureteral reflux secondary to posterior uretral valves were noted in
the fourth infant.
